A Rare Case: Herlyn-Werner-Wunderlich Syndrome

Nadir Bir Olgu: Herlyn-Werner Wunderlich Sendromu

Abstract

Herlyn-Werner Wunderlich syndrome is a rare congenital urogenital anomaly involving mullerian duct and wolfian structures. It is characterized by didelphys uterus, obstructed hemivagina and ipsilateral renal agenesis. This entity is also known as obstructed hemivagina and ipsilateral renal anomaly (OHVIRA). The clinical presentation is the mass effect and pelvic pain caused by hydrometrocolpos secondary to obstructed hemivagina. Menstruation delays the diagnosis in cases with incomplete vaginal septal. Endometriosis and pelvic adhesions are complications that can be seen in the future. Ultrasonography (USG) and Magnetik resonans imaging (MRI) are extremely useful for diagnosis.